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Table 4 Comparison of frequency of various major complications of VHL syndrome across different cohorts

From: Clinical and molecular characteristics of East Asian patients with von Hippel–Lindau syndrome

Clinical manifestation Present study Ong et al. [18] Maher et al. [4]
CNSH 81.2% (125/154) Cerebellar 57%
Spinal 25%
Cerebellar 59%
Spinal 13%
RCH 27.9% (43/154) 73% 59%
RCC 57.8% (89/154) 35% 28%
PCC 14.9% (23/154) 20% 7%
  1. CNSH central nervous system hemangioblastoma, RCH retinal capillary hemangioblastoma, RCC renal cell carcinoma, PCC pheochromocytoma
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